Rhabdomyosarcoma of biliary tract: A diagnostic dilemma

Rhabdomyosarcoma is a soft tissue malignant musculoskeletal tumor. It is a rare tumor in children but the most common cause of malignant obstructive jaundice in them. A 4-year-old child presented to us with obstructive jaundice and palpable liver. He was misdiagnosed as choledochal cyst on imaging studies; however, intraoperative and histopathological features confirmed the diagnosis of rhabdomyosarcoma. Mass excision and Roux en Y portoenterostomy was performed. Post operatively; the patient was put on multimodal chemotherapy. This, being an uncommon entity, is being reported with a review of the available literature.

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Author informationAuthors and Affiliations

Department of Pediatric Surgery, Institute of Medical Sciences, Banaras Hindu University, Varanasi, 221005, U.P., India

V. Kumar, S. Chaudhary & A. N. Gangopadhyay

Department of Pathology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, 221005, U.P., India

M. Kumar

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Correspondence to A. N. Gangopadhyay.

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Kumar, V., Chaudhary, S., Kumar, M. et al. Rhabdomyosarcoma of Biliary Tract— a Diagnostic Dilemma. Indian J Surg Oncol 3, 314–316 (2012). https://doi.org/10.1007/s13193-012-0186-7

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Received: 03 January 2012

Accepted: 04 September 2012

Published: 06 October 2012

Issue Date: December 2012

DOI: https://doi.org/10.1007/s13193-012-0186-7