Author(s): The ESMO/European Sarcoma Network Working Group
Extraskeletal Ewing sarcoma is covered by other ESMO Guidelines: in general, the same principles for these tumours in children apply to adults. This is also the case for embryonal and alveolar rhabdomyosarcoma, which are exceedingly rare in adults. On the other hand, pleomorphic rhabdomyosarcoma is viewed as a high-grade adult-type soft tissue sarcoma. Gastrointestinal stromal tumours are covered by the dedicated ESMO Clinical Practice Guidelines. Kaposi's sarcoma is excluded.
incidenceAdult soft tissue and visceral sarcomas (excluding gastrointestinal stromal tumour) are rare tumours, with an estimated incidence averaging 4–5/100 000/year in Europe
Author(s): Pariente A
Author(s): Milic DJ, Rajkovic MM, Pejcic VD
Author(s): Mehdi S, Jalil M, Said B, Mohammed KL, Rahal M, et al.
Author(s): Marudanayagam R, Sandhu B, Perera MT, Bramhall SR, Mayer D
Author(s): Choi YY, Lee IS, Kim SJ, Kim JI, Choi KU
Author(s): Honoré C, Méeus P, Stoeckle E, Bonvalot S
Author(s): Okajima Y, Nishikawa M, Ohi M, Fukumoto Y, Kuroda K, et al.
Author(s): Coindre JM, Terrier P, Bui NB, Bonichon F, Collin F, et al.
Author(s): Behranwala KA, A’Hern R, Omar AM, Thomas JM
Author(s): Pisters PW, Harrison LB, Leung DH, Woodruf JM, Casper ES
Author(s): Dufresne A, Cassier P, Heudel P, Pissaloux D, Wang Q, et al.
